Pulmonary atresia with intact ventricular septum associated with aortic coarctation
Arjamand Shauq1, Gordon Gladman, Edmund J Ladusans
1Department of Paediatric Cardiology, Alder Hey Children Hospital, Liverpool, UK. shauq7@yahoo.com
Abstract:
Pulmonary atresia with intact septum is itself a rare congenital abnormality, albeit known to be associated with other cardiac and non-cardiac anomalies. The combination of right- and left-sided obstructive lesions, however, is extremely rare. We describe a patient having pulmonary atresia with intact septum associated with aortic coarctation, which to the best of our knowledge has been previously described on but one occasion.
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