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Congenital pseudarthrosis of the clavicle
Guido Currarino1, John A Herring
1Department of Radiology, Texas Scottish Rite Hospital for Children, Dallas, TX 75219, USA. guidonellie@mac.com
Insights
Congenital pseudarthrosis of the clavicle is a rare condition primarily affecting girls, often presenting as a mid-clavicle bulge. Surgical treatment was required for most patients in this study.
Area of Science:
- Pediatric Orthopedics
- Medical Imaging
- Skeletal Dysplasias
Background:
- Congenital pseudarthrosis is a rare skeletal anomaly with limited pediatric literature.
- This condition involves the abnormal formation of a joint-like structure where bone should be continuous.
Observation:
- The study reviewed four pediatric cases of congenital pseudarthrosis of the clavicle.
- Patients were girls aged 4–14 years.
- The primary symptom was a mid-clavicle bulge; one patient had upper extremity discoloration and venous distention.
Findings:
- All four cases involved the mid-portion of the right clavicle.
- Three patients had no other congenital abnormalities.
- One 14-year-old patient also had an exostosis on her left hand.
Implications:
- Congenital pseudarthrosis of the clavicle predominantly affects girls and the right mid-clavicle.
- Early diagnosis and appropriate management, often surgical, are crucial for pediatric patients.
- Further research is needed to understand the etiology and long-term outcomes.
Background:
Congenital pseudarthrosis is an uncommon anomaly poorly referred to in the pediatric literature.
Objective:
To describe congenital pseudarthrosis in children. We discuss the presentation, clinical symptomatology, and treatment.
Materials And Methods:
We reviewed the records of four children with congenital pseudarthrosis from 1990 to 2009 at the radiology department of Texas Scottish Rite Hospital for Children.
Results:
Four girls ages 4 through 14 were identified. Three children presented with a bulge in the mid-clavicle as a chief complaint. The fourth child (14 years old) had bluish discoloration of the right upper extremity with venous distention. Three of the four did not have other abnormalities, while the 14-year-old had exostosis on the left hand. The mid-portion of the right clavicle was involved in all four children. Three of the four were treated surgically.
Conclusion:
Congenital pseudarthrosis of the clavicle is an uncommon anomaly found mostly in girls and in the mid-right clavicle.
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