Angiocentric lymphoma: a case report

A group of rare lymphoproliferative disorders, now called angioimmunoproliferative lesions, are histologically characterized by mononuclear cells surrounding and infiltrating vessel walls. This process results in angiodestruction and originates necrosis. Angiocentric lymphoma, a neoplasia generally deriving from the T cell lineage, is the most aggressive form of these entities characterized by prevalent extranodal involvement. A case of primary angiocentric lymphoma with lymph-nodel and systemic presentation and rapidly fatal outcome is described.