A case of primary cardiac angiosarcoma: extensive right atrial wall reconstruction with autologous pericardium

Primary cardiac angiosarcoma is a rare and aggressive tumor. Diagnosis is usually late because of the rarity of the lesion and the nonspecific clinical symptoms. We report the case of a 48-year-old man affected by angiosarcoma of the right atrium who presented with subacute cardiac tamponade. Extensive resection of the atrial wall infiltrated by the tumor, followed by autologous pericardial free atrial wall reconstruction, was successfully carried out. In spite of the optimal early outcome, the patient died 15 months later because of multiple osteal metastases.