A case of infantile meningioangiomatosis with a separate cyst

Seong Ho Kim1, Soo Han Yoon, Jang Hee Kim

  • 1Department of Neurosurgery, College of Medicine, Yeungnam University, Daegu, Korea.

Insights

Meningioangiomatosis (MA) is a rare pediatric tumor. This case highlights a MA with a separate cyst, suggesting non-tumor cysts may not need surgical removal.

Area of Science:

  • Pediatric Neurosurgery
  • Neuropathology
  • Congenital Neoplasms

Background:

  • Meningioangiomatosis (MA) is a rare congenital tumor typically affecting children aged 5-15.
  • Previous reports on MA have infrequently described cystic components within the tumors.

Observation:

  • A 2-year-old female presented with seizures, revealing a calcified mass with an associated cyst in the right parietal area.
  • Imaging showed edema and hemorrhage surrounding the lesion.
  • Surgical excision of the mass was performed, but the separate cyst was biopsied and left in situ due to absence of tumor tissue.

Findings:

  • Pathological examination confirmed meningioangiomatosis.
  • Two-year follow-up showed no tumor recurrence and no neurological deficits.
  • The separate cyst did not exhibit tumor infiltration.

Implications:

  • This case suggests that cysts adjacent to meningioangiomatosis may be distinct entities and not neoplastic.
  • Non-neoplastic, separate cysts may not require surgical intervention, potentially reducing patient morbidity.
  • Further investigation into the nature and management of cysts associated with MA is warranted.

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