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Extraosseous Ewing's sarcoma / primitive neuroectodermal tumor of the sacral nerve plexus
M K Narula1, Nishant Gupta, Rama Anand
1Department of Radiodiagnosis, Lady Hardinge Medical College, and Associated Smt. Sucheta Kriplani and Kalawati Saran Children Hospital, New Delhi-110 001, India.
The Indian Journal of Radiology & Imaging
|November 3, 2009
Summary
A rare Ewing sarcoma / primitive neuroectodermal tumor (PNET) was found in a child's sacral nerve plexus. Prompt treatment with chemotherapy and radiotherapy led to significant improvement.
Area of Science:
- Pediatric Oncology
- Neurosurgery
- Radiology
Background:
- Ewing sarcoma / primitive neuroectodermal tumor (PNET) is a rare and aggressive cancer.
- Sacral nerve plexus involvement is an uncommon presentation of this tumor type.
Observation:
- A 9-year-old boy presented with lower back pain and soft tissue swelling.
- MRI revealed a lobulated mass along the sacral nerves, causing spinal canal widening and vertebral changes.
Findings:
- Histopathology confirmed Ewing sarcoma / PNET of the sacral spinal nerve plexus.
- The tumor exhibited presacral extension and posterior scalloping of sacral vertebrae.
Implications:
- This case highlights the importance of considering rare tumor locations in pediatric oncology.
- Multimodal treatment including chemotherapy and radiotherapy can be effective for sacral PNET.
- Early diagnosis and intervention are crucial for favorable outcomes in pediatric neuroectodermal tumors.
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