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[Congenital nasal pyriform aperture stenosis and solitary maxillary central incisor: case report]
Jesús Gimeno-Hernández1, María C Iglesias-Moreno, Manuel Gómez-Serrano
1Servicio de Otorrinolaringología, Hospital Clínico Universitario San Carlos, Madrid, España. j.gimeno@med.ucm.es
Insights
Congenital nasal pyriform aperture stenosis, a rare condition, can cause neonatal breathing and feeding issues. This case highlights successful conservative management in an infant with this condition and a solitary central incisor.
Area of Science:
- Otolaryngology
- Pediatric Surgery
- Medical Genetics
Background:
- Congenital nasal pyriform aperture stenosis (CNPAS) is a rare condition characterized by the narrowing of the nasal aperture.
- It results from the abnormal upward growth of the maxillary bone apophysis.
- CNPAS can lead to significant neonatal respiratory distress and feeding difficulties.
Observation:
- A newborn female presented with symptoms suggestive of CNPAS.
- The infant also exhibited a rare associated anomaly: a solitary maxillary central incisor.
- A conservative management approach was selected for this case.
Findings:
- The patient was monitored closely following the diagnosis.
- After one year of observation and conservative care, the infant demonstrated appropriate physical development, including adequate height and weight gain.
- No surgical intervention was required during the observation period.
Implications:
- Conservative management can be a viable option for select cases of congenital nasal pyriform aperture stenosis.
- Early diagnosis and monitoring are crucial for managing neonates with CNPAS.
- The association with dental anomalies warrants further investigation in future studies.
Abstract:
Congenital nasal pyriform aperture stenosis has recently been described in the literature. It is caused by an upward overgrowth of the maxillary bone apophysis and may cause breathing and feeding problems from the neonatal period on. We present the case of a newborn girl diagnosed with this pathology associated with a solitary maxillary central incisor. Observation with conservative measures was the attitude chosen. One year after diagnosis the patient shows adequate height and weight development.
