Compressive effects of intravascular papillary endothelial hyperplasia

A 45-year-old woman presented with an 8-month history of a firm mass over the right superonasal orbital rim, followed by an episode of hemorrhage and anesthesia 5 months later. Clinical history and CT were suggestive of a venous malformation with phleboliths. Excision biopsy was performed. Histopathology revealed intravascular papillary endothelial hyperplasia with fibrotic-calcific changes. Hypoesthesia in the supra-orbital region persisted postoperatively. Although a benign lesion, intravascular papillary endothelial hyperplasia should be considered a differential diagnosis of a vascular lesion with compressive effects.