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Nesidioblastosis: evidence for autosomal recessive inheritance
D A Woolf1, J V Leonard, R C Trembath
1Institute of Child Health, University of London.
Archives of Disease in Childhood
|April 1, 1991
Abstract:
The risk of recurrence of nesidioblastosis is unclear. Thirty patients from 28 families were studied; the marriages were consanguineous in five families. The ratio of subsequent affected to unaffected siblings was similar to that of an autosomal recessive condition and the sex ratio was close to 1.
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