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Congenitally corrected transposition of great arteries with severe rhythm disturbances

Mehmet Kayrak1, Zeynettin Kaya, Enes Elvin Gul

  • 1Selcuk University, Meram Faculty of Medicine, Department of Cardiology, Konya, Turkey.

Indian Pacing and Electrophysiology Journal
|April 9, 2010
PubMed

Insights

Congenitally corrected transposition of the great arteries (CCTGA) can cause severe rhythm disorders. This case study highlights treatment options and implantable cardioverter-defibrillator (ICD) indications for CCTGA patients with arrhythmias.

Area of Science:

  • Cardiology
  • Adult Congenital Heart Disease
  • Electrophysiology

Background:

  • Congenitally corrected transposition of the great arteries (CCTGA) is a complex congenital heart defect.
  • CCTGA presents with atrioventricular (AV) and ventriculoarterial (VA) discordance, leading to physiological blood flow.
  • Cardiac death in CCTGA is often attributed to complete AV block and ventricular dysfunction.

Purpose of the Study:

  • To present a case of CCTGA with severe rhythm disorders.
  • To discuss potential treatment strategies for such cases.
  • To explore indications for implantable cardioverter-defibrillator (ICD) implantation in patients with congenital heart disease (CHD).

Main Methods:

  • Case report presentation.
  • Review of treatment options for CCTGA-related arrhythmias.
  • Analysis of ICD implantation criteria in CHD patients.

Main Results:

  • The case involved CCTGA with significant rhythm disturbances.
  • Various treatment modalities were considered.
  • The study provides insights into the role of ICDs in managing CCTGA complications.

Conclusions:

  • Arrhythmias are a significant cause of morbidity and mortality in CHD.
  • ICD implantation is a consideration for CCTGA patients with severe rhythm disorders.
  • Further research is needed to refine treatment guidelines for CCTGA patients.

Keywords:
arrhythmiascongenitally corrected transposition of great arteries

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