Left ventricular diverticulum and previous rhabdomyoma: an occasional detection

Gianluca Di Bella1, Rocco Donato, Sebastiano Coglitore

  • 1Clinical and Experimental Department of Medicine and Pharmacology, University of Messina, Messina, Italy.

Insights

This case report describes a rare simultaneous occurrence of a left ventricular diverticulum and a history of right ventricular rhabdomyoma. Cardiac magnetic resonance imaging was crucial for diagnosing this congenital heart abnormality.

Area of Science:

  • Cardiology
  • Medical Imaging
  • Congenital Heart Disease

Background:

  • Rhabdomyomas are the most common primary cardiac tumors in pediatric patients, often associated with tuberous sclerosis.
  • Left ventricular diverticula are rare congenital anomalies, characterized by a outpouching of the left ventricular wall.

Observation:

  • A 35-year-old patient with a history of childhood surgery for right ventricular rhabdomyoma underwent cardiac magnetic resonance (CMR).
  • CMR revealed a dilated right ventricle and a small contractile cavity in the inferior left ventricular wall, consistent with a diverticulum.

Findings:

  • This represents the first documented case of simultaneous evidence of a left ventricular diverticulum and a history of right ventricular rhabdomyoma.
  • Cardiac magnetic resonance imaging facilitated the straightforward detection of this combined congenital abnormality.

Implications:

  • Highlights the importance of advanced imaging modalities like CMR in diagnosing complex congenital cardiac conditions.
  • Suggests a potential, though unproven, association between these rare cardiac anomalies.
  • Emphasizes the need for lifelong cardiac surveillance in patients with congenital heart disease and tumors.

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