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Interim prostacyclin therapy for an isolated disconnected pulmonary artery: a case report
1Paediatric Department, Mater Dei Hospital, Disneyland, Tal-Qroqq, Malta. victor.e.grech@gov.mt.
Introduction:
Disconnected pulmonary arteries are unusual and may result in pulmonary hypertension with acute right heart failure.
Case Presentation:
We report a case of a three-month-old Asian girl who presented with heart failure and severe pulmonary hypertension due to a disconnected right pulmonary artery. An epoprostenol (prostacyclin) infusion was instrumental in lowering pulmonary artery pressures and stabilizing the child prior to surgery.
Conclusions:
This is, to the best of our knowledge, the first report of successful prostacyclin usage in such a situation.
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