Bilateral single-system ectopic ureters opening into vaginalized urogenital sinus

Area of Science:

• Pediatric Urology
• Congenital Anomalies
• Genitourinary Tract Reconstruction

Background:

• Describes a rare case of a 5-year-old female with a congenital urinary tract anomaly.
• Highlights the challenges in managing urinary incontinence and voiding dysfunction from birth.

Observation:

• Patient presented with continuous urinary dribbling and absence of a urinary stream.
• Investigations revealed bilateral single-system ectopic ureters opening into the vaginalized urogenital sinus.
• An absent urethra and coarctation of the aorta were noted as associated anomalies.

Findings:

• This represents the first reported instance of bilateral single-system ectopic ureters opening into a vaginalized urogenital sinus.
• The patient had an incontinent bladder neck and a small, dysfunctional bladder.

Implications:

• The absence of a urethra necessitates specialized management strategies.
• Continent urinary diversion should be considered due to the complex anatomy and bladder dysfunction.
• This case underscores the importance of thorough diagnostic evaluation for complex genitourinary malformations.