Successful congenital heart surgery for a toddler with idiopathic infantile arterial calcification

Margaret M Samyn1, David Bick, John A Humphrey

  • 1Herma Heart Center, Children's Hospital of Wisconsin, Milwaukee, WI, 53226, USA. msamyn@chw.org

Pediatric Cardiology
|June 17, 2010
PubMed

Insights

Idiopathic infantile arterial calcification (IIAC) is often fatal in infants. This case report details successful cardiac surgery in a 27-month-old boy with IIAC, overcoming severe pulmonary valve stenosis.

Area of Science:

  • Pediatric Cardiology
  • Cardiovascular Surgery
  • Rare Genetic Diseases

Background:

  • Idiopathic infantile arterial calcification (IIAC) is a rare genetic disorder characterized by diffuse calcification of large arteries.
  • IIAC typically presents in early infancy with a high mortality rate, often within the first six months of life.
  • Severe cardiovascular complications, such as valvular stenosis, can arise in affected infants.