[Cerebral sinus vein thrombosis in Behçet's disease]

A 20-year-old Turkish patient presented with superior sagittal sinus thrombosis which led to the final diagnosis of Behçet's disease. The frequency of cerebral venous thrombosis is generally underestimated and may be the first clinical manifestation of Behçet's disease. Uveitis as a main diagnostic criterion of Behçet's disease may be absent, especially in young men. In cases of intracranial hypertension, cerebral venous thrombosis and Behçet's disease should be taken into consideration, especially in a high risk population from eastern Mediterranean countries and Japanese islands. Treatment with early anticoagulation in cerebral venous thrombosis, and corticosteroid-pulse therapy in active Behçet's disease, seems to be established today. As a basic therapy of Behçet's disease cyclosporin A and the classic immunosuppressive agents, especially azathioprine, are available. Clinical course and prognosis in cerebral venous thrombosis are generally both benign, provided that adequate management is started in time.