Related Experiment Video
Updated: Jun 10, 2026
05:12
Portable Thermographic Screening for Detection of Acute Wallenberg's Syndrome
Published on: September 19, 2019
Wyburn-Mason syndrome: a case report
1Department of Otolaryngology, Head and Neck Surgery, University Hospital Giessen, & Marburg, Campus Marburg, Germany. swiegand@med.uni-marburg.de
B-ENT
|August 5, 2010
Summary
Wyburn-Mason syndrome, a rare arteriovenous malformation disorder, requires individualized treatment. Surgical intervention was successful in managing recurrent bleeding and complications in a presented case.
Area of Science:
- Vascular malformations
- Embryonic development
- Neurology
Background:
- Wyburn-Mason syndrome is a rare congenital condition characterized by arteriovenous malformations (AVMs) affecting the brain, orbit, and face.
- It results from an insult during embryonic development, leading to abnormal vascular development.
Observation:
- A 47-year-old male with Wyburn-Mason syndrome presented with recurrent epistaxis at the left orbit.
- Initial treatments included radiotherapy and angioembolisation, followed by surgical reduction and orbital exenteration, which reduced bleeding.
- Two years later, the patient developed maxillary sinus empyema with massive endonasal bleeding, necessitating a transorbital approach for treatment.
Findings:
- Surgical intervention, including orbital exenteration, effectively reduced bleeding episodes in this patient.
- A transorbital approach was required to manage subsequent maxillary sinus empyema due to severe bleeding complications.
Implications:
- While observation is standard for Wyburn-Mason syndrome, complex cases necessitate tailored management strategies.
- This case highlights the potential success of surgical intervention in managing symptomatic Wyburn-Mason syndrome and its complications.