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Erythrokeratodermia progressivum symmetricum
1From the Department of Dermato-Venereology, Rajindra Hospital, Patiala-147001, India, .
Indian Journal of Dermatology, Venereology and Leprology
|October 6, 2010
Summary
This case report details a rare progressive symmetric erythrokeratodermia (PSEK) in an Indian male. Diagnosis was confirmed via histopathology, distinguishing it from psoriasis.
Area of Science:
- Dermatology
- Rare Genetic Disorders
Background:
- Progressive symmetric erythrokeratodermia (PSEK) is a rare genodermatosis.
- Characterized by progressive, symmetrical, erythematous, and hyperkeratotic plaques.
Purpose of the Study:
- To report a unique case of PSEK in an Indian male.
- To highlight clinical and histopathological features for accurate diagnosis.
Main Methods:
- Clinical examination of skin lesions.
- Histopathological analysis of skin biopsy.
- Exclusion of differential diagnoses like psoriasis.
Main Results:
- The patient presented with bilateral, symmetrical plaques on limbs with erythematous halos.
- Koebner's phenomenon was observed.
- Histopathology confirmed PSEK and ruled out psoriasis.
Conclusions:
- This case expands the understanding of PSEK presentation in diverse ethnicities.
- Accurate histopathological examination is crucial for diagnosing PSEK and differentiating it from other conditions.
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