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Sporadic creutzfeldt jacob disease
Hussein A Algahtani1, Karim M Qumosani, Imad M Khojah
1Neurology Section, Department of Medicine, King Abdulaziz Medical City, PO Box 12723, Jeddah 21483, Kingdom of Saudi Arabia. Tel. +966 (2) 6240000 Ext. 21298/22070. Fax.+966 (2) 6240000 Ext. 22765.
Neurosciences (Riyadh, Saudi Arabia)
|November 11, 2010
Summary
This case report details a 65-year-old woman diagnosed with Creutzfeldt-Jacob disease (CJD), a rare neurological disorder. Recognizing CJD is crucial for diagnosing rapidly progressive dementia, especially in regions with limited reported cases.
Area of Science:
- Neurology
- Rare Diseases
- Neurodegenerative Disorders
Background:
- Rapidly progressive dementia presents a diagnostic challenge.
- Creutzfeldt-Jacob disease (CJD) is a rare, fatal neurodegenerative prion disease.
- Limited case reports of CJD exist in Saudi Arabia.
Purpose of the Study:
- To report a case of Creutzfeldt-Jacob disease (CJD) in a 65-year-old female.
- To highlight the rarity of CJD in Saudi Arabia.
- To emphasize the importance of including CJD in the differential diagnosis of rapidly progressive dementia.
Main Methods:
- Case presentation of a 65-year-old female with rapidly progressive dementia.
- Literature review of Creutzfeldt-Jacob disease (CJD) cases in Saudi Arabia.
Main Results:
- The patient was diagnosed with Creutzfeldt-Jacob disease (CJD).
- Only three previous case reports of CJD from Saudi Arabia were identified.
Conclusions:
- Creutzfeldt-Jacob disease (CJD) is a rare but critical consideration in rapidly progressive dementia.
- Increased awareness of CJD in the region is warranted for accurate diagnosis and patient management.
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