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Updated: Jun 6, 2026
04:44
Imaging Features of Systemic Sclerosis-Associated Interstitial Lung Disease
Published on: June 16, 2020
Benign spontaneous pneumoperitoneum in systemic sclerosis
John Vischio1, Zinaida Matlyuk-Urman, Santhanam Lakshminarayanan
1Division of Rheumatology, University of Connecticut Health Center, Farmington, CT, USA. johnvischio@yahoo.com
Summary
Systemic sclerosis (SSc) patients can develop benign spontaneous pneumoperitoneum, a rare condition often linked to pneumatosis cystoides intestinalis (PCI). This case highlights the importance of recognizing this non-surgical complication in SSc patients.
Area of Science:
- Gastroenterology
- Rheumatology
- Radiology
Background:
- Systemic sclerosis (SSc) frequently impacts the gastrointestinal tract, leading to motility issues, malabsorption, and diverticular disease.
- Pneumatosis cystoides intestinalis (PCI) and benign spontaneous pneumoperitoneum are rare gastrointestinal complications associated with SSc.
Observation:
- A case report details a malnourished patient with long-standing SSc presenting with spontaneous pneumoperitoneum.
- Initial CT scans revealed pneumoperitoneum and PCI, but no signs of visceral perforation or peritoneal irritation.
Findings:
- The pneumoperitoneum persisted on follow-up imaging, while the PCI resolved.
- This suggests benign spontaneous pneumoperitoneum can occur in SSc patients without acute abdominal catastrophe.
Implications:
- Clinicians must differentiate benign spontaneous pneumoperitoneum from surgically emergent conditions like perforated viscus in SSc patients.
- Supportive management is indicated for benign spontaneous pneumoperitoneum, avoiding unnecessary surgical intervention.
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