Vomerine hamartoma in a cleft palate child

Rameshwar L Bang1, Hisham Burezq, Imad Al-Najjadah

  • 1Al Babtain Centre for Burns and Plastic Surgery, Ibn-Sina Hospital Kuwait.

Insights

This case report details a rare vomerine hamartoma in a female infant with cleft palate, successfully treated with surgery. The benign tumor caused feeding issues but showed no recurrence after nine years.

Area of Science:

  • Oral and Maxillofacial Surgery
  • Pediatric Surgery
  • Pathology

Background:

  • Bilateral secondary complete cleft palate is a congenital condition affecting oral structures.
  • Vomerine hamartomas are rare benign tumors that can present intraorally.
  • Differentiating vomerine hamartomas from other midline oral masses, such as encephaloceles, is crucial for appropriate management.

Observation:

  • A female infant presented with a bilateral secondary complete cleft palate and a vomerine hamartoma.
  • The hamartoma mimicked an intra-oral midline encephalocoele but was radiologically confined to the vomer without intracranial extension.
  • The lesion obstructed the oral cavity, leading to feeding difficulties.

Findings:

  • Surgical excision of the vomerine hamartoma was performed at six months of age.
  • A two-flap palatoplasty was completed at twelve months of age.
  • Histopathological examination confirmed the lesion as a benign lipomatous hamartoma.

Implications:

  • This case represents the first reported instance of a cleft palate associated with a vomerine hamartoma in English literature.
  • Successful surgical management resulted in no recurrence over a nine-year follow-up period.
  • The patient achieved satisfactory speech outcomes post-intervention, highlighting the importance of early diagnosis and treatment.