Mixed-type total anomalous pulmonary venous connection in an adult

Zhiheng Wang1, Weibo Qi, Yi Hu

  • 1Department of Cardiothoracic Surgery, The 1st Affiliated Hospital, Jiaxing University, Jiaxing, People’s Republic of China.

Insights

This study details a rare congenital heart defect, total anomalous pulmonary venous connection, where pulmonary veins connect abnormally. Surgical repair using a pericardial patch was successful, with no complications at 5-month follow-up.

Area of Science:

  • Cardiology
  • Pediatric Cardiology
  • Congenital Heart Disease

Background:

  • Total anomalous pulmonary venous connection (TAPVC) is a rare congenital heart defect.
  • Mixed-type TAPVC involving both cardiac and infracardiac drainage is exceptionally uncommon.
  • Understanding the anatomical variations is crucial for surgical planning.

Observation:

  • A case of mixed-type TAPVC is presented, characterized by pulmonary venous confluence draining into a vertical vein.
  • This vertical vein connected to the inferior vena cava via the hepatic vein.
  • The anomaly represents a complex cardiac malformation requiring specialized surgical intervention.

Findings:

  • Successful surgical correction was achieved through deroofing the coronary sinus.
  • The interatrial septum was reconstructed using a pericardial patch.
  • The surgical approach effectively addressed the anomalous venous connection.

Implications:

  • This case highlights a viable surgical strategy for a rare TAPVC variant.
  • Successful outcomes demonstrate the feasibility of complex congenital heart defect repair.
  • Further research into surgical techniques for rare cardiac anomalies is warranted.

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