Mixed-type total anomalous pulmonary venous connection in an adult
Zhiheng Wang1, Weibo Qi, Yi Hu
1Department of Cardiothoracic Surgery, The 1st Affiliated Hospital, Jiaxing University, Jiaxing, People’s Republic of China.
Insights
This study details a rare congenital heart defect, total anomalous pulmonary venous connection, where pulmonary veins connect abnormally. Surgical repair using a pericardial patch was successful, with no complications at 5-month follow-up.
Area of Science:
- Cardiology
- Pediatric Cardiology
- Congenital Heart Disease
Background:
- Total anomalous pulmonary venous connection (TAPVC) is a rare congenital heart defect.
- Mixed-type TAPVC involving both cardiac and infracardiac drainage is exceptionally uncommon.
- Understanding the anatomical variations is crucial for surgical planning.
Observation:
- A case of mixed-type TAPVC is presented, characterized by pulmonary venous confluence draining into a vertical vein.
- This vertical vein connected to the inferior vena cava via the hepatic vein.
- The anomaly represents a complex cardiac malformation requiring specialized surgical intervention.
Findings:
- Successful surgical correction was achieved through deroofing the coronary sinus.
- The interatrial septum was reconstructed using a pericardial patch.
- The surgical approach effectively addressed the anomalous venous connection.
Implications:
- This case highlights a viable surgical strategy for a rare TAPVC variant.
- Successful outcomes demonstrate the feasibility of complex congenital heart defect repair.
- Further research into surgical techniques for rare cardiac anomalies is warranted.
Abstract:
Cardiac plus infracardiac mixed-type total anomalous pulmonary venous connection is an extremely rare congenital heart disease. We describe a case in which the pulmonary veins made a confluence and connected to a vertical vein running into the inferior vena cava by the way of the hepatic vein. Surgical correction was successfully obtained by deroofing the coronary sinus and using the pericardial patch to reconstruct the interatrial septum. The patient showed no signs of any complication at her 5-month follow-up.
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