Malignant peripheral nerve sheath tumor of mandible

Malignant peripheral nerve sheath tumor is a common tumor that rarely affects the head and neck region. The patient presented in this report is a teenage girl presented with a lesion in the right body of the mandible with severe disfigurement of the lower face. The lesion was first histopathologically diagnosed as embryonal rhabdomyosarcoma. After excision, however, the histopathology report proved the diagnosis of malignant peripheral nerve sheath tumor.