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Published on: September 20, 2018
Behçet disease in children
Leyla Atmaca1, Ayse Boyvat, F Nilüfer Yalçındağ
1Department Ophthalmology, Ankara University Medical School, Ankara, Turkey. leylaatmaca@ttmail.com
Ocular Immunology and Inflammation
|March 25, 2011
Summary
Behçet disease in children is rare, affecting 3.3% of patients, with ocular involvement common. Early diagnosis and multidisciplinary care are crucial for managing this childhood uveitis condition.
Area of Science:
- Pediatrics
- Ophthalmology
- Rheumatology
Background:
- Behçet disease is a rare multisystemic inflammatory disorder.
- Childhood-onset Behçet disease requires specific diagnostic considerations.
Purpose of the Study:
- To determine the incidence and clinical features of Behçet disease in pediatric patients.
- To highlight the importance of considering Behçet disease in childhood uveitis.
Main Methods:
- Retrospective chart review of 3382 Behçet disease patients from 1986-2005.
- Analysis focused on 110 diagnosed pediatric cases.
Main Results:
- Children constituted 3.3% of all Behçet disease patients reviewed.
- Ocular involvement was present in 30.9% of pediatric cases, with uveitis being a common manifestation.
- The mean age at onset was 11.6 years and at diagnosis was 14.1 years, with a female predominance (62.7%).
Conclusions:
- Behçet disease is an important differential diagnosis for childhood uveitis, especially in endemic regions.
- Multidisciplinary collaboration among pediatricians, rheumatologists, ophthalmologists, and dermatologists is essential for accurate diagnosis and management.
- Prompt recognition and management can improve outcomes for children with Behçet disease.
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