Gastrointestinal reconstruction and outcomes for patients with the OEIS complex

The OEIS complex (ie, omphalocele-exstrophy-imperforate anus-spinal defects) is a rare and complex anomaly requiring collaboration among multiple pediatric surgical subspecialties throughout the early childhood period. Initial gastrointestinal management involves identification of all intestinal components with reconstruction of the entire length of intestines in-line leading to an end colostomy. Candidacy for an abdominoperineal intestinal pull-through procedure is dependent upon the patient's ability to form solid stools, degree of pelvic neuromuscular development, and ability to comply with a bowel management program.