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Beevor's sign and facioscapulohumeral dystrophy.
G I Awerbuch1, M A Nigro, R Wishnow
1Children's Hospital of Michigan, Detroit 48201.
Archives of Neurology
|November 1, 1990
Summary
Beevor's sign is a common indicator in patients with facioscapulohumeral dystrophy (FSHD). This simple screening test can help differentiate FSHD from other neuromuscular conditions, even before significant muscle weakness is evident.
Area of Science:
- Neurology
- Clinical Diagnostics
- Genetics
Background:
- Facioscapulohumeral dystrophy (FSHD) is a progressive muscle disorder.
- Early and accurate diagnosis of FSHD is crucial for patient management.
- Distinguishing FSHD from other neuromuscular diseases can be challenging.
Purpose of the Study:
- To investigate the diagnostic value of Beevor's sign in patients with FSHD.
- To compare the prevalence of Beevor's sign in FSHD versus other neuromuscular disorders.
- To assess Beevor's sign as an early screening tool for FSHD.
Main Methods:
- Prospective evaluation of 30 patients diagnosed with FSHD.
- Evaluation of 40 patients with various other neuromuscular disorders as controls.
- Systematic assessment for the presence or absence of Beevor's sign in all participants.
Main Results:
- Beevor's sign was present in 27 out of 30 (90%) patients with FSHD.
- Beevor's sign was absent in all 40 (0%) control patients with other neuromuscular disorders.
- The sign was observed even in FSHD patients without apparent abdominal muscle weakness.
Conclusions:
- Beevor's sign is a highly prevalent clinical finding in FSHD.
- This sign can be a useful, simple screening test for identifying potential FSHD cases.
- Testing for Beevor's sign may aid in differentiating FSHD from other neuromuscular syndromes.