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Updated: Jun 2, 2026

Invasive Hemodynamic Characterization of the Portal-hypertensive Syndrome in Cirrhotic Rats
Published on: August 1, 2018
[Subclinical acute intermittent porphyria. An uncommon cause of chronic hepatitis]
Juan Pérez Martínez1, Cristina Castro Márquez, Sofía Pereira Gallardo
1Servicio de Aparato Digestivo, Hospital Universitario Virgen Macarena, Sevilla, España.
Abstract:
Acute porphyria is a term that encompasses a group of hereditary disorders involving defects in heme metabolism, characterized by acute episodes of abdominal pain, acute hypertension, tachycardia and neuropsychiatric disorders, sometimes leading to convulsions, ascending paralysis and coma. Misdiagnosis or delayed diagnosis can seriously worsen prognosis. We report the case of a woman with subclinical acute intermittent porphyria and chronic hepatitis incidentally diagnosed due to transaminase elevation on laboratory analysis.
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