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A case of right sided aortic arch combined with atrial septal defect

Geun Jin Ha1, Myeung Joon Sung, Young Soo Lee

  • 1Department of Cardiology, Catholic University of Daegu School of Medicine, Daegu, Korea.

Journal of Cardiovascular Ultrasound
|April 27, 2011
PubMed

Insights

Right-sided aortic arch, a rare congenital condition, can coexist with heart defects. This case highlights successful surgical repair in an 18-year-old female with an atrial septal defect and associated conditions.

Area of Science:

  • Cardiology
  • Congenital Heart Disease
  • Vascular Anomalies

Background:

  • Right-sided aortic arch (RSAA) is a rare congenital anomaly with varied classifications based on aortic arch degeneration and great vessel branching.
  • RSAA can be associated with significant congenital heart disease, with prevalence and type dependent on the specific RSAA classification.
  • Understanding these associations is crucial for diagnosis and management.

Observation:

  • A case report of an 18-year-old female presenting with a right-sided aortic arch.
  • The patient exhibited an aberrant left subclavian artery, an atrial septal defect (ASD) of the ostium secundum type, moderate tricuspid regurgitation, and pulmonary hypertension.
  • These findings represent a complex constellation of cardiovascular anomalies.

Findings:

  • The patient's right-sided aortic arch was associated with an atrial septal defect (ostium secundum) and moderate tricuspid regurgitation.
  • Pulmonary hypertension was noted, indicating significant hemodynamic impact.
  • Surgical intervention involved successful patch closure of the ASD and tricuspid valve annuloplasty.

Implications:

  • This case underscores the importance of recognizing the potential for associated cardiac defects in patients with right-sided aortic arch.
  • Timely diagnosis and surgical correction of congenital heart disease, such as ASD, in the context of RSAA can lead to favorable outcomes.
  • The successful management highlights the efficacy of surgical repair in improving patient prognosis.

Keywords:
Atrial septal defectRight sided aortic arch

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