Primary hemangiopericytoma of bone - a case-report and literature-review
R Spagnolo1, L Torelli, R Brusamolino
1IST NAZL TUMORI,DIV SURG ONCOL B,VIA GIACOMO VENEZIAN 1,I-20133 MILAN,ITALY. OSPED NIGUARDA CA GRANDA,PIAZZA OSPED MAGGIORE,DIV ORTOPED & TRAUMATOL,MILAN,ITALY. OSPED NIGUARDA CA GRANDA,PIAZZA OSPED MAGGIORE,IST ANAT PATOL,MILAN,ITALY. IST NAZL TUMORI,DIV ONCOL CHIRURG & DIAGNOST,I-20133 MILAN,ITALY.
Abstract:
Clinical, radiological and histological aspects of a case of primary bone haemangiopericytoma, treated by wide surgical resection and pre- and postoperative radiotherapy, are described. The patient was disease-free 20 months from the operation. From a literature review of 52 cases of this very rare tumour it emerges that the tumour is aggressive but of variable malignancy. Prognosis seems to depend on histology, size at diagnosis and treatment. The best available treatment is probably wide exeresis plus radiotherapy.
