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Primary pigmented micronodular disease of the adrenals
P Limone1, M Maccario, R Vigliani
1Istituto di Medicina Interna, Università di Torino, Italy.
Journal of Endocrinological Investigation
|February 1, 1990
Abstract:
Primary pigmented micronodular disease is a peculiar form of ACTH-independent Cushing's syndrome characterized by the familial occurrence, the frequent association with malformations and the pathological adrenocortical picture consisting in micronodules with cellular deposition of lipofuscinic pigment. We describe here a case occurring in a 14-year-old girl.
Insights
Primary pigmented micronodular disease, a rare cause of Cushing's syndrome, presents with adrenal micronodules and pigment deposition. This summary details a case in a 14-year-old girl.
Area of Science:
- Endocrinology
- Pathology
Background:
- Primary pigmented micronodular disease (PPMMD) is a rare endocrine disorder.
- It is characterized by ACTH-independent Cushing's syndrome, familial occurrence, and specific adrenocortical pathology.