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Growing a Cystic Fibrosis-Relevant Polymicrobial Biofilm to Probe Community Phenotypes
03:53

Growing a Cystic Fibrosis-Relevant Polymicrobial Biofilm to Probe Community Phenotypes

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[Cystic fibrosis, a paradigm for modern medicine]

Jean-Marie Tschopp1

  • 1Centre valaisan de pneumologie, Département de médecine interne, CHCVs, 3963 Montana. jean-marie.tschopp@hopitalvs.ch

Revue Medicale Suisse
|May 21, 2011
PubMed

Insights

Cystic fibrosis (CF) care has improved significantly, increasing median survival to 38 years. This progress stems from comprehensive, multidisciplinary approaches and patient advocacy, enhancing CF visibility and support.

Area of Science:

  • Genetics and Medicine
  • Pediatric Disorders
  • Chronic Disease Management

Context:

  • Cystic fibrosis (CF) is a severe genetic disorder affecting Caucasian children.
  • Historically, CF patients had poor survival rates, often succumbing in childhood.
  • Significant advancements in care have dramatically improved patient prognosis.

Purpose:

  • To highlight the evolution of cystic fibrosis care.
  • To underscore the impact of multidisciplinary approaches and patient advocacy.
  • To present CF as a model for chronic disease management.

Summary:

  • Cystic fibrosis (CF) is the most common severe genetic disorder in Caucasian children, impacting multiple organ systems.
  • Median survival for CF patients has risen to 38 years due to comprehensive care.
  • Progress is attributed to scientific research, multidisciplinary clinical teams, and early patient organization support.

Impact:

  • Improved survival rates and quality of life for cystic fibrosis patients.
  • Enhanced societal visibility and support for CF.
  • CF serves as a paradigm for advancing the care of chronic diseases across medicine.

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