Female covered urethral duplication with urogenital sinus
Pascale Philippe-Chomette1, Smart Zeidan, Nadia Belarbi
1Department of Pediatric Surgery and Urology, AP-HP, Robert Debré University Hospital, University of Paris Diderot, Paris, France.
Abstract:
We report a covered urethral duplication in a girl presenting prenatally with an enlarged fluid-filled vulvar cyst, genital duplication, and urogenital sinus revealed by fetal magnetic resonance imaging (MRI) and serial ultrasounds. Physical examination revealed an enlarged vulvar mass covering the clitoris, a single orifice, and normally sited anus. Congenital adrenal hyperplasia was ruled out at birth. MRI in addition showed an accessory duct between the sinus and the urine-filled vulvar pouch with a bifid clitoris. A total urogenital sinus mobilization with resection of the accessory urethra and vulvoplasty was performed with uneventful follow-up.
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