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Updated: Jun 1, 2026

Granulocyte-dependent Autoantibody-induced Skin Blistering
Published on: October 12, 2012
[Weber-Christian disease: unknown etiology systemic panniculitis]
Anabela Oliveira1, Sandra Rodrigues, Rosa Jorge
1Serviço de Medicina, Hospital Infante D. Pedro, Aveiro.
Abstract:
Panniculitis is an inflammation occurring within adipose tissue. This process is often associated with auto-immune diseases, infections, malignancy and others diseases of unknown cause. We report a 16-year-old woman with constitutional symptoms and relapsing nonsuppurative nodular panniculitis. The etiological study didn't identify any associated disease, on admission or in 2,5 years of follow-up. This is a case of Weber-Christian disease with a favourable corticosteroid therapy result. The authors present a Weber-Christian disease bibliographic revision.
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