Coronary artery-left ventricular microfistulae associated with apical hypertrophic cardiomyopathy

Ozgül Uçar1, Hülya Ciçekçioglu, Mustafa Cetin

  • 1Department of Cardiology, Ankara Numune Education and Research Hospital, Talatpaşa Bulvari, Sihhiye, Ankara, Turkey.

Cardiology Journal
|June 11, 2011
PubMed

Insights

A rare combination of coronary artery microfistulae and apical hypertrophic cardiomyopathy presented with angina pectoris. Beta-blocker therapy effectively alleviated symptoms in this unique case.

Area of Science:

  • Cardiology
  • Cardiovascular Medicine
  • Medical Imaging

Background:

  • Coronary artery to left ventricular microfistulae are rare vascular anomalies.
  • Apical hypertrophic cardiomyopathy is a distinct form of hypertrophic cardiomyopathy.

Observation:

  • A 58-year-old man presented with angina pectoris and ECG changes (ST depression, inverted T waves).
  • Coronary angiography identified widespread coronary artery to left ventricular microfistulae.
  • Left ventriculography and echocardiography confirmed apical hypertrophic cardiomyopathy.

Findings:

  • The patient exhibited a rare co-occurrence of coronary artery microfistulae and apical hypertrophic cardiomyopathy.
  • Angina pectoris symptoms were successfully managed with beta-blocker medication.

Implications:

  • This case highlights the importance of considering rare conditions in complex cardiovascular presentations.
  • Further research into the pathophysiology and clinical management of this combined condition is warranted.
  • Understanding this rare combination may improve patient outcomes and therapeutic strategies.

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