Leiomyosarcoma arising from the inferior mesenteric vein
Gennaro Clemente1, Gerardo Sarno, Brunella Barbaro
1Catholic University, Department of Surgery, Largo Gemelli 8, Rome, 00168, Italy.
BMJ Case Reports
|June 21, 2011
Summary
A rare inferior mesenteric vein leiomyosarcoma was incidentally discovered in a 66-year-old woman. Early diagnosis and surgical excision led to a favorable prognosis, with no recurrence after 24 months.
Area of Science:
- Vascular Oncology
- Gastrointestinal Surgery
- Rare Tumors
Background:
- Leiomyosarcomas originating from the portal/mesenteric venous system are exceptionally rare.
- Vascular leiomyosarcomas are generally associated with a poor prognosis.
- Literature reports on inferior mesenteric vein leiomyosarcomas are scarce.
Purpose of the Study:
- To report a rare case of leiomyosarcoma of the inferior mesenteric vein.
- To discuss the clinical presentation, diagnosis, and management of this rare entity.
- To review the existing literature on vascular leiomyosarcomas of the mesenteric system.
Main Methods:
- Case report of a 66-year-old female patient.
- Incidental diagnosis during a computed tomography (CT) scan for an unrelated indication.
- Radical surgical excision of the tumor.
Main Results:
- The patient was diagnosed with leiomyosarcoma of the inferior mesenteric vein.
- The tumor was unexpectedly discovered via CT scan.
- Following radical surgical excision, the patient remained disease-free with no radiological signs of recurrence at 24 months post-surgery.
Conclusions:
- Early incidental diagnosis and prompt treatment likely contributed to a favorable prognosis in this case.
- This represents the second reported case of leiomyosarcoma of the inferior mesenteric vein in the literature.
- Aggressive surgical management may be effective for localized inferior mesenteric vein leiomyosarcomas.
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