[Primary giant pulmonary leiomyosarcoma]

The authors describe their case of primary giant pulmonary leiomyosarcoma as a rare cancer nosological entity. The specific features of the case were not only its rarity, the extent of lung and mediastinal involvement, and the pattern of tumor growth, but also the absence of metastases despite aggressive course. The size of the tumor and its specific growth pattern determined technical surgical treatment problems and early postoperative complications that resulted in death.