Complete recovery following sudden sensorineural hearing loss in a patient with sickle cell disease

A sickle cell disease (SCD) patient with vaso-occlusive crisis (VOC) developed sudden senserinural hearing loss (SNHL), which responded well to a rapid course of corticosteroids along with exchange transfusions. The otolaryngologist should be aware of the otologic manifestations of SCD such as SNHL. A good response to steroids, which averted a permanent hearing loss, warrants further studies to define the augmentive benefits of such therapy along with exchange transfusions in patients with SCD in VOC who develop sudden SNHL.