Isolated double-chambered right ventricle in a young adult

Jung-Gil Park1, Han-Jun Ryu, Yeun-Su Jung

  • 1Department of Internal Medicine, Daegu Fatima Hospital, Daegu, Korea.

Insights

Double-chambered right ventricle (DCRV), a rare congenital heart defect, can be asymptomatic in adults. This case highlights diagnosis using echocardiography, cardiac catheterization, and MRI.

Area of Science:

  • Cardiology
  • Congenital Heart Disease
  • Adult Congenital Heart Disease

Background:

  • Double-chambered right ventricle (DCRV) is a rare congenital anomaly.
  • It involves anomalous muscle bundle division of the right ventricle into high-pressure inlet and low-pressure outlet portions.

Purpose of the Study:

  • To report a case of isolated DCRV.
  • To describe the diagnosis of asymptomatic adult DCRV.

Main Methods:

  • Echocardiography
  • Cardiac catheterization
  • Cardiac magnetic resonance imaging (CMR)

Main Results:

  • Isolated DCRV was diagnosed in an adult.
  • The patient was asymptomatic.

Conclusions:

  • DCRV can remain undiagnosed into adulthood.
  • Advanced imaging and hemodynamic assessment are crucial for diagnosing DCRV.

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