Aspiration pneumonia in the child with DiGeorge syndrome -A case report-

Ji-Young Lee1, Yun-Joung Han

  • 1Department of Anesthesiology and Pain Medicine, St. Mary's Hospital, The Catholic University of Korea College of Medicine, Seoul, Korea.

Insights

DiGeorge syndrome, a 22q11.2 deletion disorder, presents risks like aspiration pneumonia during surgery. This case highlights successful management of perioperative aspiration pneumonia in a child with DiGeorge syndrome undergoing cranioplasty.

Area of Science:

  • Medical Case Report
  • Pediatric Surgery
  • Genetics

Background:

  • DiGeorge syndrome is a genetic disorder caused by a deletion on chromosome 22q11.2.
  • Patients with DiGeorge syndrome exhibit diverse clinical manifestations.
  • Perioperative aspiration pneumonia is a significant concern in individuals with this syndrome.

Purpose of the Study:

  • To report a case of perioperative aspiration pneumonia in a child with DiGeorge syndrome.
  • To illustrate the successful management of this complication.
  • To emphasize the importance of vigilance in managing patients with DiGeorge syndrome.

Main Methods:

  • Case presentation of a 16-month-old child with DiGeorge syndrome.
  • Description of the surgical procedure (cranioplasty).
  • Details of the management of aspiration pneumonia.

Main Results:

  • The patient developed perioperative aspiration pneumonia.
  • The aspiration pneumonia was successfully managed.
  • The patient recovered from the complication.

Conclusions:

  • Perioperative aspiration pneumonia is a manageable complication in DiGeorge syndrome.
  • Successful management is crucial for patient outcomes.
  • This case underscores the need for careful perioperative planning and monitoring.

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