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Cantrell syndrome with complex cardiac malformations: a case report

Li Wen1, Liao Jun-lin, Hao Jia

  • 1Department of Radiology, XinQiao Hospital, Third Military Medical University, ChongQing 400037, PR China.

Journal of Pediatric Surgery
|July 19, 2011
PubMed

Insights

Cantrell syndrome, a rare congenital defect affecting five structures, presents significant survival challenges. This case highlights successful surgical intervention and positive long-term outcomes for a patient with this complex condition.

Area of Science:

  • Pediatric Surgery
  • Congenital Malformations
  • Cardiology

Background:

  • Cantrell syndrome is a rare congenital defect involving the abdominal wall, sternum, diaphragm, pericardium, and heart.
  • It is associated with high mortality and poor quality of life for survivors.

Observation:

  • A male infant presented with Cantrell syndrome and severe cardiac malformations.
  • The patient experienced multiple life-threatening events but survived to undergo surgical repair at 5 months old.

Findings:

  • Surgical intervention successfully reduced the cardiac size within the thoracoabdominal cavity.
  • The abdominal wall defect was repaired, and multiple stenoses of the heart and great vessels were addressed.

Implications:

  • This case demonstrates the feasibility of complex surgical repair for Cantrell syndrome.
  • Successful outcomes are possible, leading to a normal, healthy development in survivors.

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