The sirenomelia sequence: a case history

Anis Fadhlaoui1, Mohamed Khrouf, Soumaya Gaigi

  • 1Department of Gynecology and Obstetrics, Aziza Othmana Hospital, Place du Gouvernement, La Kasba, Tunis, Tunisia.

We report a case of sirenomelia sequence observed in an incident of preterm labor during the 29th gestational week. According to some authors, this syndrome should be classified separately from caudal regression syndrome and is likely to be the result of an abnormality taking place during the fourth gestational week, causing developmental abnormalities in the lower extremities, pelvis, genitalia, urinary tract and digestive organs. Despite recent progress in pathology, the etiopathogenesis of sirenomelia is still debated.

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