Thrombosed congenital extrahepatic portal vein aneurysm in an infant

Yang Wen1, Hyun Woo Goo

  • 1Department of Radiology, Beijing Children's Hospital Affiliated to Capital Medical University, Beijing, China.

Pediatric Radiology
|July 21, 2011
PubMed

Insights

Extrahepatic portal vein aneurysm is rare in infants. A congenital case in an infant showed complete regression on follow-up ultrasound after 16 months.

Area of Science:

  • Pediatric Surgery
  • Vascular Anomalies
  • Diagnostic Imaging

Background:

  • Extrahepatic portal vein aneurysm (EHPVA) is an exceptionally rare condition, particularly in infants.
  • Congenital EHPVA presents a diagnostic and management challenge due to its rarity.

Observation:

  • A case report details an infant diagnosed with a thrombosed congenital extrahepatic portal vein aneurysm.
  • Diagnosis was confirmed using ultrasound (US) and computed tomography (CT) imaging.

Findings:

  • The infant's thrombosed congenital extrahepatic portal vein aneurysm demonstrated significant regression.
  • Follow-up US after 16 months revealed complete resolution of the portal vein aneurysm.

Implications:

  • This case highlights the potential for spontaneous regression of congenital extrahepatic portal vein aneurysms in infants.
  • It underscores the importance of serial imaging in managing these rare vascular anomalies.
  • Further research may elucidate the natural history and optimal management strategies for pediatric EHPVA.

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