Enteric duplication cyst of the pancreas with duplicated pancreatic duct

Jun Fujishiro1, Michio Kaneko, Yasuhisa Urita

  • 1Department of Pediatric Surgery, University of Tsukuba, Tsukuba, Ibaraki, 305-8575, Japan. jfujishi@md.tsukuba.ac.jp

Insights

This case report details a rare enteric duplication cyst of the pancreas communicating with a duplicated pancreatic duct in a child. Surgical excision was successful, highlighting the need for considering this rare condition in pancreatic cyst diagnoses.

Area of Science:

  • Gastroenterology
  • Pediatric Surgery
  • Surgical Pathology

Background:

  • Enteric duplication cysts are rare congenital anomalies, infrequently involving the pancreas.
  • Pancreatic cystic lesions present a diagnostic challenge, especially in pediatric patients.
  • Accurate diagnosis is crucial for appropriate management and surgical planning.

Observation:

  • A 7-year-old girl presented with severe acute abdominal pain.
  • Imaging revealed a large pancreatic cyst communicating with a dilated pancreatic duct in the pancreatic tail.
  • Cyst fluid analysis showed elevated amylase, CEA, and CA 19-9, with no epithelial cells.

Findings:

  • Intraoperative cyst pancreatography confirmed a duplicated pancreatic duct in the tail.
  • One duct communicated with the cyst, while the other was dilated.
  • The patient underwent successful spleen-preserving distal pancreatectomy and cyst excision.

Implications:

  • Preoperative diagnosis of pancreatic enteric duplication cysts is challenging.
  • This rare condition should be included in the differential diagnosis of pancreatic cystic lesions.
  • Complete surgical excision is the recommended management for pancreatic duplication cysts.

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