Modified bjork procedure for tricuspid atresia with pulmonary hypertension

Tricuspid atresia (TA) is a rare and life-threatening cyanotic congenital heart anomaly, which is traditionally treated by the Fontan procedure. However, this procedure may be limited by the development of pulmonary hypertension and lead to long-term complications. The Bjork procedure offers an alternative for biventricular repair and right ventricular growth, especially in patients with pulmonary hypertension. We report a case of TA with pulmonary hypertension successfully treated with the modified Bjork procedure using an aortic homograft valved conduit.