Levoatriocardinal vein with normal intracardiac anatomy and pulmonary venous return

Area of Science:

• Cardiology
• Pediatric Cardiology
• Congenital Heart Disease

Background:

• Levoatriocardinal vein (LACV) is a rare congenital heart malformation.
• It typically involves abnormal pulmonary and systemic venous return, often with left-sided obstructive lesions.
• Associated conditions include mitral atresia and hypoplastic left-heart syndrome, leading to low cardiac output and pulmonary venous obstruction.

Observation:

• This report presents an extremely rare case of LACV.
• The patient exhibited normal pulmonary venous return and no intracardiac pathology.
• Diagnosis was confirmed using echocardiography, angiography, and computed tomography.

Findings:

• A unique presentation of Levoatriocardinal vein (LACV) was identified.
• Absence of associated left-sided obstructive lesions or intracardiac anomalies was noted.
• Successful surgical correction of the LACV was achieved.

Implications:

• This case expands the understanding of LACV spectrum.
• It highlights the possibility of LACV without typical associated anomalies.
• Successful surgical outcomes are possible even in atypical presentations, emphasizing the importance of accurate diagnosis.