Cor triatriatum and coronary artery fistula in tetralogy of Fallot

Girish Meenahalli Palleda1, Mohit D Gupta, Sanjay Tyagi

  • 1Department of Cardiology, GB Pant Hospital, New Delhi, India.

Insights

Diagnosing a rare congenital heart defect, divided left atrium with tetralogy of Fallot, is challenging. This case highlights successful preoperative identification of this complex association, including a coronary fistula.

Area of Science:

  • Cardiology
  • Congenital Heart Disease
  • Cardiac Surgery

Background:

  • Tetralogy of Fallot (TOF) is a complex congenital heart defect.
  • Divided left atrium (DLA) is an extremely rare anomaly.
  • The coexistence of DLA and TOF presents significant diagnostic and therapeutic challenges.

Observation:

  • This report details a rare case of a patient presenting with both DLA and TOF.
  • Preoperative diagnosis of this combined anomaly was achieved.
  • The patient also exhibited an unusual coronary artery fistula to the left ventricle.

Findings:

  • Successful preoperative diagnosis of the rare DLA-TOF association was established.
  • The presence of a coronary to left ventricle fistula was identified preoperatively.
  • This case underscores the importance of advanced imaging in diagnosing complex congenital heart conditions.

Implications:

  • Accurate preoperative diagnosis is crucial for planning surgical intervention in complex congenital heart disease.
  • Recognition of rare anatomical variations like DLA in TOF patients can alter surgical strategy.
  • Understanding these rare associations aids in improving patient outcomes and surgical planning.

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