Deformity of the tongue in an infant: Riga-Fede disease

Karen A Eley1, Pauline A Watt-Smith, Stephen R Watt-Smith

  • 1Department of Plastic Surgery, Oxford Radcliffe Hospitals NHS Trust, Oxford;

Insights

Riga-Fede disease is a rare oral ulceration in infants caused by tongue trauma from teeth. Prompt diagnosis and management, including potential tooth extraction, ensure healing and prevent recurrence.

Area of Science:

  • Pediatric Dentistry
  • Oral Pathology

Background:

  • Riga-Fede disease is a rare benign condition characterized by ulceration of the lingual tissues.
  • It results from repetitive trauma by teeth in children under two years old.

Observation:

  • An 11-month-old girl presented with a significant tongue tip defect due to ulceration.
  • The ulceration was attributed to trauma from her teeth.

Findings:

  • Excisional biopsy of the lesion resulted in complete healing.
  • No recurrence of the ulceration was observed post-biopsy.

Implications:

  • Riga-Fede disease should be considered in the differential diagnosis of oral ulcerations in infants.
  • Conservative management or tooth extraction may be necessary for persistent cases or those with failure to thrive.

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