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Updated: May 27, 2026

Multimodality Diagnosis of Mesenteric Ischemia
Published on: July 21, 2023
A fatal case of Degos' disease which presented with recurrent intestinal perforation
Mona Ahmadi1, Sevil Agabalaey Rafi, Zhale Faham
1Mona Ahmadi, Sevil Agabalaey Rafi, Zhale Faham, Ramin Azhough, Samad Beheshty Rooy, Omid Rahmani, Department of General Surgery and Pathology, Imam Reza Hospital, Azadi Street, Tabriz 5156975389, Iran.
Abstract:
Degos' disease, otherwise known as "malignant atrophic papulosis" is a rare vasculopathy with an unknown etiology characterized by typical cutaneous lesions. Involvement of the gastrointestinal (GI) tract is observed in approximately half of patients and small infarctions in the mucosa can cause perforation and resulting peritonitis, the leading cause of death. We present a fatal case of Degos' disease with skin and GI involvement, manifesting as recurrent intestinal perforations and peritonitis, in a 15-year-old Iranian boy.
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