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[Pulmonary sequestration and enteric cyst, 2 expressions of the same abnormality]

Q Ballouhey1, F Brémont, J-L Rittié

  • 1Service de chirurgie pédiatrique, hôpital des enfants, 330, avenue de Grande-Bretagne, TSA 70034, 31059 Toulouse cedex 9, France. q.ballouhey@gmail.com

Archives De Pediatrie : Organe Officiel De La Societe Francaise De Pediatrie
|December 16, 2011
PubMed

Insights

A child with bronchopulmonary sequestration developed a thoracic effusion and a mediastinal cyst. Resection revealed an enteric cyst, highlighting the importance of searching for both conditions when one is found.

Area of Science:

  • Pediatric Surgery
  • Thoracic Surgery
  • Congenital Abnormalities

Background:

  • Bronchopulmonary sequestration is a rare congenital lung malformation.
  • Enteric cysts are rare congenital anomalies, typically found in the mediastinum or abdomen.
  • The co-occurrence of these two conditions is exceptionally uncommon.

Observation:

  • An 18-month-old boy underwent surgery for right lower lobe bronchopulmonary sequestration.
  • Postoperatively, he developed a septic right thoracic effusion linked to a cystic mediastinal retrocrural formation.
  • Imaging revealed a connection between the thoracic effusion and the mediastinal cyst.

Findings:

  • Despite drainage and medical management, the abdominal lesion required resection.
  • Histological examination confirmed the cyst was an enteric cyst, lacking cartilage and lined with pseudostratified non-ciliated epithelium.
  • This finding suggests a potential shared embryological origin or a complex developmental relationship.

Implications:

  • The case underscores the critical need to investigate for associated anomalies when diagnosing either bronchopulmonary sequestration or enteric cysts.
  • Systematic screening for the presence of one lesion when the other is identified is crucial for comprehensive patient management.
  • This approach can prevent delayed diagnosis and improve patient outcomes in pediatric surgical cases involving these rare congenital malformations.

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