Otic capsule dysplasia: clinical and CT findings

Many congenital dysplasias of the osseous labyrinth have been identified. Differentiation of these dysplasias is essential for patient management. High-resolution computed tomography (CT) was used to identify individual malformations in 32 patients. Thirty patients had six previously described forms, while two patients had a form that has not previously been reported to our knowledge. Review of patient histories revealed clinical characteristics that were specific for certain forms of otic capsule dysplasia. CT enabled detailed analysis of each lesion and helped direct proper treatment of each patient. The characteristic CT appearance and clinical presentation of each form of dysplasia are presented.