Intralobar pulmonary sequestration supplied by an anomalous aneurysmal artery
Kohei Ando1, Takamitsu Maehara, Hiroyuki Adachi
1Department of Respiratory Surgery,Yokohama Rosai Hospital, and Department of Surgery, Yokohama City University, Yokohama-city, Japan. undo0815@yahoo.co.jp
The Annals of Thoracic Surgery
|December 22, 2011
Summary
This study presents a rare case of intralobar pulmonary sequestration in a 52-year-old man with an associated aneurysmal systemic artery. The authors propose clearer nomenclature for this condition to improve diagnostic clarity.
Area of Science:
- Cardiovascular Medicine
- Thoracic Surgery
- Radiology
Background:
- Pulmonary sequestration is a congenital lung malformation characterized by non-functional lung tissue with systemic arterial supply.
- Intralobar pulmonary sequestration, a subtype, typically involves abnormal lung tissue within the visceral pleura of a normal lung lobe.
- Aneurysmal dilatation of the systemic artery supplying pulmonary sequestration is exceptionally uncommon.
Observation:
- A 52-year-old male presented with intralobar pulmonary sequestration.
- The sequestration was supplied by a significantly dilated, aneurysmal systemic artery.
- Diagnostic imaging confirmed the presence of abnormal lung tissue and the vascular anomaly.
Findings:
- The case highlights the extreme rarity of pulmonary sequestration coexisting with an aneurysmal systemic artery.
- The findings underscore the variability in vascular anatomy associated with pulmonary sequestration.
- The abnormal lung tissue received its entire blood supply from the aneurysmal systemic artery.
Implications:
- Accurate diagnosis and classification of pulmonary sequestration are crucial for appropriate management.
- The proposed nomenclature revision aims to enhance clarity and differentiate specific subtypes.
- Understanding these rare vascular associations is vital for surgical planning and preventing complications like hemorrhage.
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